Intracranial Hypertension Revealing Neuro-Behçet Disease With Favourable Outcome After Ventriculoperitoneal Shunt

Abstract

A 39-year-old man had been diagnosed after rolling out all the other possible causes as having intracranial hypertension with bilateral papilledema secondary to Behçet’s disease with normal MRI scan. Despite treatment with steroids, methylprednisolone and repetitive LPs, he had little to no improvement. The patient later underwent a ventriculoperitoneal shunt operation with corticosteroid therapy and adjuvant treatment with topiramate and acetazolamide, which resulted in symptoms improvement. Thus, it is important to consider NBD in the differential diagnosis of patients with intracranial hypertension and bilateral papilledema and also ventriculoperitoneal shunting as an effective therapeutic alternative when medical treatment fail to normalize the intracranial hypertension building up