Hydranencephaly in an Infant: About a Case at Medical Imaging for All (IMT) in Kinshasa/The Democratic Republic of Congo

Abstract

Hydranencephaly corresponds (in its major and bilateral form) to the total ischemic destruction (most often occurring between 3 and 6 months of pregnancy) of the normally developed cerebral hemispheres which are replaced by a vast liquid cavity surrounded by the meninges.However, there are the basal ganglia, the brainstem and the cerebellum.We report and describe a case of an infant, aged 9 months received in Medical Imaging for All for a brain scan on macrocephaly.In the CT-scan, we note the absence of the cerebral hemispheres replaced by LCS, without peripheral cortical plate except at the medial part of the temporal lobes, constituting a cerebral water pocket.The thalamus, cerebellum, brain stem and falx cerebri are intact.The residual temporal and occipital lobes.Exaggerated opening of the fontanelles.We concluded with hydranencephaly and we completed by transcranial ultrasound.We find an anechoic aspect of the cranial cavity, the presence of the falx of the brain; the persistence of cerebral remnants in the occipital region, medial of the temporal lobes vascularized by the anterior and posterior cerebral arteries and their anastomoses, the posterior fossa, the tent of the cerebellum, the basal nuclei and the brainstem which are preserved; the cranial vault is deformed with macrocephaly by continuous production of LCS.