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article · Urology Case Reports

Bilateral pheochromocytomas with locally advanced right adrenal tumor extending into the inferior vena cava in a suspected Von Hippel–Lindau syndrome: A case report

Abstract

We report a case of bilateral pheochromocytomas in a 45-year-old man with cutaneous findings suggestive of a hereditary disease. Imaging revealed a large right adrenal tumor extending into the inferior vena cava (IVC) and a smaller contralateral lesion. The patient underwent right adrenalectomy with IVC thrombectomy, while the left lesion was managed conservatively. Histopathology confirmed pheochromocytoma with extensive IVC tumor thrombus and no distant metastases. A residual IVC thrombus was treated with anticoagulation and remained stable on follow-up imaging. This case highlights the complexity of managing hereditary pheochromocytomas with vascular invasion.

Research topics

  • Adrenal and Paraganglionic Tumors
  • Cardiac tumors and thrombi
  • Cancer, Hypoxia, and Metabolism

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DOI: 10.1016/j.eucr.2026.103343

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