A Successful Single-Stage Reconstruction of an Isolated Female Epispadias in a 14-Year-Old Patient: A Case Report and Literature Review

Abstract

Epispadias is a rare congenital disorder characterized by an abnormal dorsal opening of the urethra due to the failure of the urethral plate to tubularize. It is usually part of broader conditions like bladder or cloacal exstrophy and rarely occurs in isolation. We present the case of a 14-year-old girl with isolated epispadias who had lifelong urinary incontinence without urgency. Genital examination revealed a bifid clitoris, underdeveloped labia minora, and a widely open urethral meatus with continuous leakage of urine. Urethrocystoscopy showed a short, patulous urethra, a poorly coapting external sphincter, and an open bladder neck. She underwent a successful single-stage surgical repair consisting of urethroplasty, bladder neck reconstruction, and perineoplasty. Two weeks after surgery, following catheter removal, the patient achieved urinary continence. This case supports the effectiveness of single-stage reconstruction even in delayed presentations of isolated female epispadias.