A Rare Localization of Solitary Neurofibroma: A Case Report

Abstract

Neurofibromas are benign connective tissue tumors that develop mainly at the expense of the endoneurium of peripheral nerves. The head and neck region is one of the sites of neurogenic tumors such as neurofibromas. Usually part of a neurofibromatosis, solitary localization in the naso-sinus cavities is rare, estimated at 4% of head and neck localizations. We report the case of an 8-year-old child hospitalized in our department for a nasal tumor, radiographic Images revealed a nasoethmoidal tumor with right orbital extension and bilateral temporoparietal schizencephaly with open cleft. Despite its rarity, solitary neurofibroma must be taken into account in the differential diagnosis of a unilateral benign tumour of the naso-sinus cavities.