A late-onset arrhythmogenic right ventricular cardiomyopathy unveiled by supraventricular tachycardia: Case report

Abstract

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a rare myocardial genetic disease that leads to heart failure and sudden cardiac death. The diagnosis of ARVC remains challenging given its variable presentation. A 66-year-old woman was admitted to our cardiac intensive care unit for the management of a left heart failure flare-up with an atrial flutter, which remains an atypical mode of the revelation of arrhythmogenic right ventricular cardiomyopathy (ARVC) retained based the association of genetic predisposition, the presence of repolarization abnormalities on electrocardiogram (EKG), the occurrence of an episode of sustained ventricular tachycardia and imaging data. ARVC is a condition with varying expressions, severity, and progression. Early detection, careful monitoring, and appropriate management are crucial in improving outcomes for individuals with ARVC.